Case presentation

A 32-year-old woman presented with a unilateral small brown blaschkoid sessile and pedunculated papules on the right side of her abdomen in the past 4 years. She did not complain from any symptom except for occasional pruritus. The lesions appeared during her first pregnancy and became more prominent and increased in number during her second pregnancy. Past medical history and examination were otherwise unremarkable.
On dermoscopic examination multiple round and oval brown pigmented circles with irregular borders and some smaller circles were seen in a homogenous light brown background(Fig 1).
Histology examination revealed a thick orthokeratosis, papillomatosis, coarse keratohyalin granules, and some vacuolated cells with dark basophilic nuclei known as epidermolytic hyperkeratotic pattern. Some superficial lymphocytic infiltration was also noted in the dermis. Regarding the history, clinical manifestation and histopathologic findings diagnosis of epidermolytic hyperkeratotic EN was made (Fig 2).