The Gerbode defect is a special type of ventricle septum defect causing a communication between the left ventricle and right atrium. In this article, we present a rare case of 2-year-old congenital Gerbode defect. The location of this defect was special, just at the interventricular septum between the tricuspid and mitral valve. She underwent the closure of the defect with an autologous pericardial patch in station of mild hypothermic cardiopulmonary bypass.