Aortic atresia
Aortic atresia is frequently associated with mitral atresia in the
context of a hypoplastic left heart and will be discussed below.
Isolated aortic atresia constitutes a rare cardiovascular anomaly. This
cardiac condition can occur with a ventricular septal defect and a
normal left ventricular size, but this occurrence is very rare and is
almost ever accompanied by a perforate mitral valve53.
Additional (severe) mitral regurgitation has been shown to carry a
rather poor prognosis54. Aortic atresia uncommonly can
complicate AV septal defects, univentricular hearts or transposition of
the great arteries55.