Introduction:
Pulmonary artery sarcomas (PASs) are the most common primary tumors of the pulmonary artery (PA), but the incidence of this diagnosis is extremely rare. PASs is predominantly presented among patients from their third to seventh decade, with an average age of 49 years. PASs are always highly malignant, women are involved twice as often as men. The most common clinical manifestation of PASs is dyspnea (72%) followed by chest pain (45%), cough (42%), and hemoptysis (24%). Systematic symptoms of PASs are less rare and they include weight loss (21%), syncope (9%), and fever (8%). The presence of these symptoms often causes misdiagnosis of pulmonary thromboembolism (PTE) (1-3).