Background
‘Classical’ echocardiographic signs of Fabry cardiomyopathy (FC), such
as left ventricular hypertrophy (LVH), posterolateral strain deficiency
(PLSD) and papillary muscle hypertrophy may have a limited diagnostic
accuracy in clinical practice.
Our aim was to evaluate the diagnostic value of left atrial (LA) strain
impairment compared to ‘classical’ echocardiographic findings to
discriminate FC.