Comment
Pulmonary artery aneurysms are found in approximately 1 in 14,000 autopsies, with most being asymptomatic, but some causing symptoms that can develop life-threatening complications.4 Many times, patients with pulmonary artery aneurysms have other cardiac or large vessel anomalies, but there are few cases reported on isolated pulmonary valve disease in association with pulmonary artery aneurysms.4, 5 Our patient is unique due to her Alpha-1 Antitrypsin Deficiency. She successfully underwent replacement of her pulmonary artery aneurysm with an interposition graft without complications.