Introduction:
The internal jugular vein (IJV) is a significant factor leading to
venous drainage from intracranial components, draining blood from the
head and neck region. The absence of an internal jugular vein (IJV) is
an asymptomatic, relatively unusual vascular abnormality (1). In the
general community, 0.05%-0.25% of people have developmental venous
abnormalities (2).
Vascular tumors (hemangioma, hemangioendotelioma, and angiosarcoma) and
vascular malformations (hemangioma, hemangioendotelioma, and
angiosarcoma) are two types of vascular malformations (3). Even though
developmental venous anomalies (DVAs) are generally thought to be
innocuous vascular malformations (4), We have met patients with symptoms
of headache as DVAs features.
Internal jugular vein absence is a unique congenital condition. Only a
few cases (in the low double digits) of a missing internal jugular vein
have been described in English literature to our awareness. Most cases
were discovered by chance during a routine check before central venous
cannulation in patients who received major surgery. We report a
32-year-old male with left internal jugular vein agenesis who has
experienced a dull headache for more than 20 years and who has no family
history of the condition. There was not yet a remarkable intervention
for this situation.