Introduction:
The internal jugular vein (IJV) is a significant factor leading to venous drainage from intracranial components, draining blood from the head and neck region. The absence of an internal jugular vein (IJV) is an asymptomatic, relatively unusual vascular abnormality (1). In the general community, 0.05%-0.25% of people have developmental venous abnormalities (2).
Vascular tumors (hemangioma, hemangioendotelioma, and angiosarcoma) and vascular malformations (hemangioma, hemangioendotelioma, and angiosarcoma) are two types of vascular malformations (3). Even though developmental venous anomalies (DVAs) are generally thought to be innocuous vascular malformations (4), We have met patients with symptoms of headache as DVAs features.
Internal jugular vein absence is a unique congenital condition. Only a few cases (in the low double digits) of a missing internal jugular vein have been described in English literature to our awareness. Most cases were discovered by chance during a routine check before central venous cannulation in patients who received major surgery. We report a 32-year-old male with left internal jugular vein agenesis who has experienced a dull headache for more than 20 years and who has no family history of the condition. There was not yet a remarkable intervention for this situation.