1 | INTRODUCTION
Atrial aneurysm is rare in cardiac anomaly, most of which are left
atrial aneurysms in adults.
Right
atrial appendage aneurysms (RAAAs) are extremely rare compared to other
cardiac aneurysms, especially for infants and pediatric population.
According to the literature, no more than 25 cases have been reported so
far, among which only 3 cases are infants or
neonates.1,2 A systematic review published in 2014
found that the highest morbidity of RAAAs was in the third decade of
life, with cases noted from the perinatal period to 72 years of
age.3 RAAAs usually involve free walls and atrial
appendages, most have congenital origins and develop in the course of
pregnancy.2,4 Generally, patients with RAAA are
usually asymptomatic and are diagnosed incidentally or until they
present some clinical symptoms like arrhythmia or
dyspnea.5 Pulmonary thromboembolism is a common
complication due to blood stasis in the
aneurysm.6However, there is no guideline for the treatment of this condition, and
surgical resection is safe and can be performed through sternotomy with
or without cardiopulmonary bypass for symptomatic
patients.2,5 Here, we reported an infant with a giant
RAAA and severe symptoms who underwent surgical resection of the
aneurysm.