ICD-10 codes likely specific for ILD/DLD diagnosis Diagnosis
D18.0 Pulmonary capillary hemangiomatosis
D86.0 Sarcoidosis of lung
I78.8 Isolated pulmonary capillaritis
J42 Bronchiolitis Obliterans (or Follicular Bronchiolitis)
J67.9 Hypersensitivity pneumonitis due to unspecified organic dust
J70.1 Radiation-induced pulmonary fibrosis
J82.81 Chronic eosinophilic pneumonia
J84.01 Pulmonary Alveolar Proteinosis
J84.02 Pulmonary alveolar microlithiasis
J84.03 Idiopathic pulmonary hemosiderosis
J84.09 Other alveolar and parieto-alveolar conditions
J84.10 Pulmonary fibrosis
J84.117 Desquamative interstitial pneumonitis
J84.83 Surfactant dysfunction due to genetic disorder
J84.841 Neuroendocrine cell Hyperplasia of Infancy
J84.842 Pulmonary Interstitial Glycogenosis
J84.843 Alveolar capillary dysplasia with vein misalignment
J84.848 Other interstitial lung diseases of childhood
J84.89 Interstitial lung disease due to systemic disease
J84.9 Interstitial pulmonary disease, unspecified
J98.4 Diffuse lung disease
M05.10 Diffuse interstitial rheumatoid disease of lung
M33.01 Juvenile dermatomyositis with pulmonary involvement
Q33.8 Congenital pulmonary alveolar capillary dysplasia
Z87.09 History of interstitial lung disease
ICD10 codes potentially associated with ILD/DLD* Diagnosis
D71 Chronic Granulomatous Disease
D72.1 Eosinophilic disorder
D81.9 Severe Combined Immunodeficiency Disease
D83.9 Common Variable Immunodeficiency
E70.331 Hermansky Pudlak Syndrome
E75.19 GM1 Gangliosidosis
F45.8 Restrictive lung disease
G11.3 Ataxia Telangiectasia
I27.23 Pulmonary veno-occlusive disease
I77.6 Vasculitis
J18.9 Inflammation of lung
J47.9 Bronchiectasis without acute exacerbation
J98.2 Interstitial emphysema
K50.90 Crohn’s disease
M08.20 Juvenile idiopathic arthritis, systemic onset
M30.1 Eosinophilic granulomatosis with polyangiitis
M61.10 Fibrodysplasia ossificans progressiva
Q33.0 Congenital cystic lung
Q82.4 Ectodermal dysplasia
R04.89 Pulmonary hemorrhage
R91.1 Lesion of lung
R93.89 Abnormal chest CT
T14.90XA Inhalation injury
T66.XXXS Radiation injury, sequela
U07.0 E-cigarette or vaping use-associated lung injury
Z94.81 S/P allogeneic bone marrow transplant
Z94.84 History of peripheral stem cell transplant