CONCLUSION
IgG4-SC is a steroid-sensitive immune-mediated fibroinflammatory disorder that should be considered as one of the differentials in patients with biliary strictures. The clinical and the radiographical findings of this disease might mimic that of cholangiocarcinoma but low levels of tumor markers and high levels of serum IgG4 should prompt consideration of IgG4-SC, as this entity responds well to medical therapy thus, obviating the need for surgery.