Conclusion:
this case report highlights the challenges in diagnosing and managing alpha-ketoglutarate dehydrogenase deficiency. It emphasizes the importance of considering metabolic disorders in the differential diagnosis of infantile seizures. The findings of this case report add to the existing literature on this rare condition and provide valuable insights into the diagnosis and management of this disorder. Further research is needed to improve the understanding of alpha-ketoglutarate dehydrogenase deficiency’s pathophysiology and identify more effective diagnostic and therapeutic interventions for this condition.