DISCUSSION:
In the above clinical case, we present a patient initially referred to our unit due to the finding of a hemangioma-type vascular tumor located at the cervical level, which is consistent with what has been reviewed in the literature as the site of greatest clinical presentation of these lesions. On the other hand, we were also able to identify that the vascular component of the hemangioma in the clinical case came from a connection to a persistent left superior vena cava, which constitutes a vascular anomaly never previously described in any case report according to what was reviewed in the literature.
In the only previously reported case of a persistent hemangioma with a connection to the left superior vena cava, it presented as an intracardiac lesion in the right atrial wall that also seemed to involve part of the interatrial groove. This condition is also a very rare presentation since cardiac hemangiomas correspond to only 1-2% of cardiac tumors and there is no report of a similar communication (14).
The fetal death that occurred in the clinical case could be presumed to be associated with the presence of the extracardiac malformation associated with PLSVC, remembering that the presence of isolated PLSVC could not be related to an increase in adverse perinatal outcomes (5). This corresponds to the fact that the observed survival rate in infants with PLSVC alone was significantly higher than that of infants with PLSVC associated with cardiac and extracardiac abnormalities in a prospective cohort study (10).