INTRODUCTION
Primary sarcomas comprise 0.8 to 2.7% of all renal tumors in
adults1. Among renal sarcomas, leiomyosarcoma (LMS)
accounts for 50-60% of all cases. It occurs more frequently in females
and typically manifests between the 40s and 60s. The most common signs
and symptoms are like those of renal cell carcinoma (RCC), mainly pain,
palpable mass, and hematuria, all of which are indicators of an
extensive local disease1.
Imaging may not always differentiate between leiomyosarcomas and renal
cell carcinomas in all patients2. It has a significant
propensity for local recurrence and often metastasizes to distant
organs3.
Adhering to Surgical CAse REport (SCARE) guidelines, we report a case of
primary renal LMS extending into the renal vein in a 31-year-old woman
patient managed with nephrectomy and adjuvant
chemotherapy4.