Key clinical message
Primary renal leiomyosarcoma is a rare but highly aggressive tumor with
a poor prognosis. Early detection and surgical excision provide the most
effective initial treatment. However, vigilant postoperative
surveillance is critical due to the elevated risk of tumor recurrence
and metastasis, as seen in this case. Keywords: case
report; renal; leiomyosarcoma; malignancy; sarcoma.