FIG 2 Lung histology of 9mo with ACD/MPV. (a) Representation of a
hypertrophic arterial wall (Ar) in hematoxylin and eosin and (b)
Verhoeff stained. (c) Representation of the misaligned pulmonary veins
(V) adjacent to the lymphatic vessel (L) and (d) alveolar dysplasia of
the lung parenchyma (Alv) in Verhoeff stained. (e) Hematoxylin-eosin
illustration of the misaligned pulmonary veins (V) and (g) alveolar
dysplasia (Alv) adjacent to the thickened pulmonary arteriole (Ar) in
(f) Verhoeff stained. (g, h) Hematoxylin-eosin and immunostaining for
CD31 (brown color) highlighting a reduced number of alveolar capillary
endothelial cells located away from the inner side of the alveoli
(arrows) in ACD/MPV (i) Hematoxylin and eosin illustration of the
alveolar dysplasia at high magnification.(j) Transmission electron
microscopy showing abnormal lamellar bodies (Lb) in alveolar epithelial
cells of alveolar dysplasia. The 1.5 cm straight line corresponds to
magnifications of (a,e) 500; (f,g) 200; (b,d,h) 100; (i) 50 and (j) x
15.000.
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