not-yet-known not-yet-known not-yet-known unknown Introduction: Xanthogranulomatous epithelial tumor (XGET) is a newly described mesenchymal neoplasm of indolent and rather locally aggressive biological behavior that arises in soft tissue and bone. Here, we present a case of XGET along with a comprehensive review of previously reported cases in the literature. Through this case report, we aim to contribute to the limited body of literature on XGET, highlighting its diagnostic challenges and management strategies. The histological diagnosis requires meticulous pathological examination and immunohistochemical staining to differentiate it from other xanthomatous lesions and spindle cell sarcomas. To our knowledge, only eight cases have been reported so far (Table 1 ). 1,2,4 The tumor was detected in different locations, involving the lower extremities and trunk. One case carried HMGA2-NCOR2 gene fusion.2 All eight cases showed keratin expression that is not usually seen in fibrohistiocytic tumors. In this case report, we describe a case of Xanthogranulomatous epithelial tumor arising in the right acetabulum bone with emphasis on its clinical and radiological follow-up after one year of the given diagnosis.