Key Clinical Message:-
Hailey- Hailey disease is a rare genodermatosis due to mutation in a gene that encodes calcium pumps, required for intracellular calcium homeostasis and transport. It poses a diagnostic dilemma for its rarity and similarity to other flexural skin lesions. This is a case of a 470 year old male with a history of intermittent pruritic lesions affecting flexural areas. We talk about the diagnosis, management and outcome of the case.
Key words:- Genodermatosis, Hailey- Hailey Disease, Calcium Pump, Familial Benign Pemphigus