Methods:-
Based on the inconclusive findings, a biopsy was performed from the lesion present in the left groin, and the histomorphology was studied, which revealed epidermal hyperplasia and hyperkeratosis along with extensive keratinocyte acantholysis, giving dissipated brick wall appearance, as well as presence of suprabasilar cleft forming vesicles.(Figure 2.A and 2.B).The histomorphological features were found to be consistent with Familial Benign Pemphigus(Hailey-Hailey Disease). Based on clinical as well as histomorphological findings, the patient was diagnosed to have Benign Familial Pemphigus (Hailey-Hailey disease).