1. INTRODUCTION:
Hailey-Hailey disease(HHD), also known as familial benign chronic
Pemphigus is a rare genodermatosis, which is inherited in an autosomal
dominant pattern with variable expressivity[1]. It is characterized
by recurrent plaques, vesicles and fissures primarily around the
intertriginous areas[2]. Hailey-Hailey disease occurs as a result of
mutations in the ATP2C1 gene, which is responsible for encoding
intracellular calcium pumps responsible for calcium ion regulation and
transport[3].The diagnosis of Hailey- Hailey disease is made through
a combination of pertinent history, characteristic clinical morphology
and histopathological findings[4]. Here, we report a case of
a-47-years old male with HHD affecting intertriginous areas.