Incidental detection of accessory mitral valve in adolescent with Atrial
Septal Defect: Diagnosis with 3D Transesophageal Echocardiography and
Excision with Transaortic Method
Abstract
Background: Accessory mitral valve tissue (AMVT) is an
extremely rare causes left ventricular outflow tract (LVOT) obstruction
and is usually incidentally detected in childhood. It is often
associated with other cardiac and vascular congenital malformations.
Case Presentation: In this case, we present a 15-year-old girl
was diagnosed with AMVT by transesophageal echocardiography, resulting
in LVOT obstruction during systole. Interestingly enough, the patient’s
accessory mitral valve remained undetected for years until he became
symptomatic for wide ASD. Successful closure of the ASD with resection
of the AMVT was performed with a transaortic approach. The patient was
hemodynamically stable postoperatively. There were no abnormalities in
the mitral valves and LVOT. Conclusion: It was also unusual to
see AMVT with ASD instead of other frequently associated other
congenital anomalies. Accessory mitral valve should be considered a rare
but important cause of left ventricular outflow tract obstruction in
childhood.