Successful Surgical Management of Aortopulmonary window with Severe
Pulmonary Artery Dilatation causing compression of Left Main Coronary
Artery in an Adolescent
Abstract
Aortopulmonary Window is a rare congenital heart defect comprising
0.1-0.2% of the total spectrum. Spontaneous closure of this defect is
unknown and survival into childhood and adult life is rarely seen.
Severe pulmonary artery hypertension develops and causes dilatation of
the pulmonary artery. Left main coronary artery extrinsic compression by
an enlarged pulmonary artery is a rare complication and a potential
cause for chest pain and sudden cardiac death in patients with pulmonary
hypertension.