Abstract
The multisystemic manifestations of cystic fibrosis (CF) involve all
parts of the gastrointestinal (GI) system, including the pancreas,
intestine and liver. As providers who care for people with CF (PwCF),
knowledge of the manifestations, treatment and research related to
nutrition and GI disease is important. This review is last installment
of the CF Year in Review 2020 series, focusing on the multisystem
effects of CF. Part one focused on the literature related to CFTR
(cystic fibrosis transmembrane conductance regulator protein)
modulators, while part two focused on pulmonary outcomes, radiographic
and physiologic assessments, as well as infection and inflammation. Part
three was split into Part 3A, focusing on the multisystem impact of CF,
and this review, Part 3B, focusing on nutritional, gastrointestinal and
hepatobiliary articles. Articles were chosen from Pediatric Pulmonology
but also include articles published in 2020 from other journals that are
of particular interest to clinicians.