The arterial switch operation (ASO) is the procedure of choice for the management of d-transposition of the great arteries (TGA). However, the surgical management of infants older than 6 weeks with TGA and intact ventricular septum (IVS) remains contentious. We report a case of late presenting TGA, IVS with Systolic anterior motion(SAM) of mitral valve with preserved left ventricle(LV) and its management.