Pulmonary vein isolation after partial pulmonary vein repair in patient
with heterotaxy, anomalous right pulmonary veins and atrial fibrillation
with associated cardiomyopathy
Abstract
Partial anomalous pulmonary venous connection (PAPVC) is an unusual
congenital anomaly with variable sites of attachment of the atypical
pulmonary veins. Anomalous right pulmonary vein return can be surgically
corrected if left to right shunt physiology becomes hemodynamically
significant. In such patients, as in the general population, the
development of arrhythmia-associated heart failure due to atrial
fibrillation prompts consideration of pulmonary vein isolation. There
are limited reports of pulmonary vein isolation on surgically repaired
PAPVC. This case highlights successful isolation of surgically corrected
right pulmonary veins in a patient with PAPVC and atrial fibrillation
associated heart failure.