In this case, we reported an old female with a rare combination of the Scimitar Syndrome and pulmonary artery aneurysm, and she presented with chest pain, fatigue and shortness when admitted in our hospital. Further cardiac examination including echocardiography and computed tomography angiogram were performed and revealed these rare anomalies. Surgical procedure was carried out to cure the patient. This patient stayed in ICU for few days without any major complications and discharged from hospital after 10 days.