Cardiac involvement of hydatid cyst disease is a rare presentation but may lead to life-threatening complications such as cyst rupture and should be treated surgically A 10-year-old male patient with cranial and complicated cardiac hydatid cyst disease lesions that caused lower extremity peripheral arterial occlusion and aneurysmatic dilatation in the left ventricular apex is presented. Although the patient was in the pediatric age group, the Dor procedure was successfully applied to preserve the ventricular geometry. The Dor procedure for a ventricular aneurysm caused by a cardiac hydatid cyst was rarely applied in the pediatric age group. Inconclusion, this case differs from other cardiac hydatid cysts previously reported in the literature due to the advanced stage of the disease, atypical clinical presentation, and rare complications despite the young age of the case. The surgical method used in treating the patient makes the subject more interesting.