Regression of kaposiform lymphangiomatosis and chronic disseminated intravascular coagulation after inhaled budesonide-formoterol treatmentMasaru Imamura1, Chansu Shin1, Akihiko Saitoh1, Michio Ozeki 2, Kentaro Matsuoka3 Chihaya Imai11Department of Pediatrics, Niigata University Graduate School of Medical and Dental Sciences, Niigata, Japan2Department of Pediatrics, Graduate School of Medicine, Gifu University, Gifu, Japan3Department of Pathology, Tokyo Metropolitan Children’s Medical Center, Tokyo, JapanCorresponding author: Masaru Imamura, Department of Pediatrics, Niigata University Graduate School of Medical and Dental Sciences, 1-757 Asahimachi-dori, Chuou-ku, Niigata City, Niigata 951-8510, Japan.Phone +81-25-227-2222FAX +81-25-227-0778Email: [email protected] Count for Main Text: 701 wordsNumber of Tables: 0Number of Figures: 2Running title: KLA IMPROVED AFTER INHALED STEROIDKeywords: kaposiform lymphangiomatosis, lymphatic malformation, inhaled corticosteroid, rare disease, progressive diseaseAbbreviations: