INTRODUCTION:Necrobiosis lipoidica (NL) is a relatively rare granulomatous skin disorder, associated with dermal collagen degeneration. When develops in the context of diabetes, it is specifically referred to as necrobiosis lipoidica diabeticorum (NLD).Skin involvement is commonly characterized by well-defined brownish-yellow indurated plaques with overlying telangiectasias, violaceous borders and atrophic center. It mainly affects the pretibial area but can also present in the upper extremities, trunk, genitalia, face and scalp (1, 2).Moreover, morphea (also known as localized scleroderma), is a rare and self-limited autoimmune skin disorder of excess collagen production and deposition, causing inflammation and fibrosis of dermis and subcutaneous tissues. Plaque type morphea as the most common form of localized scleroderma, initially presents as slightly elevated, reddish or purplish plaques that gradually expand outward in a centrifugal pattern. In the later stages of the disease, skin lesions develop into dyspigmented, atrophic and sclerotic plaques. Commonly involved areas include the trunk, as well as the inframammary and inguinal regions.Both necrobiosis lipoidica and morphea are non-infectious inflammatory dermatoses of unclear pathogenesis and etiology(1, 3). As of now, only four cases of concurrent necrobiosis lipoidica (NL) and morphea have been documented in the literature. One case was detailed in a case report, while the other three were included in a retrospective study (4, 5). Herein, we document a case of concomitant NL and morphea in a 43-year-old non-diabetic woman with a history of NL on her elbow, recently developed a plaque-type morphea on her trunk. We also review the literature on other dermatoses that have been reported to coexist with NL.