Introduction:Less than 10% of people with vasculitis experience cardiac impairment; however, all primary vasculitides can target the heart1. Regarding antineutrophil cytoplasmic antibody (ANCA)-associated vasculitis, both granulomatosis with polyangiitis (GP), microscopic polyangiitis (MP), and eosinophilic granulomatosis with polyangiitis (EGPA) can affect any cardiac tissue 1.Among ANCA-associated vasculitis, EGPA is the one that most frequently affects the heart 2. Nevertheless, in EGPA, cardiac manifestations are more common in ANCA-negative patients. Eosinophilic myocarditis is the most common, but restrictive or dilated cardiomyopathy, pericarditis, coronary artery vasculitis, valvular defects, rhythm disturbances, left ventricular dysfunction, and intracardiac thrombosis, among other things, can also occur3. Heart involvement in GP and MP is seen in a small percentage of patients, with pericarditis and supraventricular arrhythmias being the most common cardiac manifestations, occurring in 1% to 6% of patients 1. Nevertheless, cardiac thrombosis is a less frequent manifestation, occurring in less than 1% of patients 1.