Introduction:Primary Sjögren’s syndrome(pSS) is an idiopathic, autoimmune disorder characterized by both localized and systemic manifestations. The most common clinical presentations include the “sicca” or “dryness” symptoms such as xerostomia and keratoconjunctivitis sicca due to diminished salivary gland and lacrimal gland function, respectively. Patients may also present with nonspecific symptoms such as fatigue and arthralgia, as well as pulmonary, gastrointestinal, neurological and renal involvement.1 Secondary Sjogren’s syndrome can coexist with other autoimmune disorders such as rheumatoid arthritis (RA) and systemic lupus erythematosus (SLE). 2According to literature, ocular signs and symptoms in pSS range from foreign body sensations, punctate or filamentous keratitis, to overt seborrheic blepharitis and eyelid swelling is reported to be rare.3 We report an usual/rare presentation of Sjogren’s syndrome in which the patient developed severe evolving mechanical ptosis and eyelid swelling to the extent that it impaired her ability to lift open her eyes and see, along with a positive anti-acetylcholine receptor antibody test.
